Anotia is a rare hereditary malformation that causes complete absence of the auricle, the outer part is referred as 'Pinna' and lack of external auditory meatus. 'Auditory Meatus' has two passages one is ear drum and other for blood vessels and nerves. This disease may cause conductive hearing loss, deafness.
The human ear divided into three specialized functional regions.
This is only disease not connected with syndrome, of anotia is not known, although it is supposed to be of hereditary basis. Anotia/Microtia disease causes the ear when the certain tissues connected with the auricle do not develop. This kind of defect takes place due to a part of syndrome or as an isolated abnormality. This rare defect may occur as part of a syndrome.
Type I: External portion of the ear is small and the auricle keeps possession of most of its usual structure.
Type II: The external ear is quite abnormal and can be hook, ‘S’ or ‘?’ shaped in appearance.
Type III: The external is a basic soft tissue structure with no cartilage; the earlobe does not have a usual form.
Type IV: Anotia is that type of disease where in all structures of external ear are not present.
The treatment varies from patient to patient, but the most common method used to treat anotia is surgical repair. It reconstructs the ear's normal shape and repairs the canal of the ear. Bone Anchored Hearing Aid (BAHA) surgery is used to restore the hearing.